A phenylalanine-free powdered medical food for the dietary management of phenylketonuria (PKU) in older children and adults,including pregnant women and women of child-bearing age.
Contains
a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements
XPhe
Maxamum provides 40 g of protein equivalent per 100 g of
powder
Available
as unflavored or a pleasant orange flavored powder
Does
not contain fat thereby allowing greater flexibility in modifying
energy intake
Age-appropriate formulation
Available in cans or sachets
Indications:
Phenylketonuria
Directions
for Preparation and Use:
Maxamum must be consumed in conjunction with natural protein, fluid and
other nutrients in quantities prescribed by a physician or dietitian
to meet protein and general nutrient requirements.
The
recommended intake of Maxamum will vary depending
on the age, bodyweight and medical condition of the individual.
Intake should be adjusted to maintain normal growth and development.
For accuracy, Maxamum should be weighed on a
gram scale. The daily intake of Maxamum should
be divided into equal portions and distributed throughout the
day.
Maxamum is best served with meals. Make a paste of the prescribed amount
of powder with a small volume of chilled water. Gradually add
sufficient water to make the desired volume. It is recommended
that Maxamum be prepared at a 1 to 7 dilution
(e.g. 35 g (approx ¼ cup) of powder plus 245 mL (approx.
8 fl oz) of water) and advanced to a 1 to 5 dilution (e.g. 35
g (approx ¼ cup) of powder plus 175 mL (approx. 6 fl oz)
of water). These dilutions are guidelines only. Maxamum may be given in a more concentrated form (e.g. drink or paste).
If so, water or diluted drinks should be offered at the same time.
For best taste, consume immediately. Larger volumes of prepared
drink mix should be refrigerated and used within 24 hours or preparation.
Household
Measurement
Weight
1
Cup
145
g
1/2
Cup
70
g
1/4
Cup
35
g
1
Tbsp
9
g
Precaution:
Must only be consumed
by individuals with proven phenylketonuria while under
strict medical supervision. Not intended for children
under nine years of age. Not suitable as a sole source
of nutrition. Not for parenteral use.
Storage:
Store unopened can at room temperature. Do
not store at extreme temperatures. Once opened, reseal can
and store in a cool, dry place (not in refrigerator) and use
within one month.
MacDonald A. Diet and Phenylketonuria: Time for Change? J Hum Nutr Diet. 1994; 7:105-114.
Wardley BL & Taitz LS Clinical Trial of a Concentrated Amino Acid Formula for Older Patients with Phenylketouria (XP Maxamum). Eur J Clin Nutr. 1988; 42:81-86.
Taitz LS, et al. Zinc and Selenium Levels in Older Children with Phenylketonuria – Correction of Low Plasma Levels by a New Dietary Supplement Formulation (XP Maxamum). Data on file.
Metabolics
